Sturge-Weber-syndrome with extreme ocular manifestation and rare association of upper airway angioma with anticipated difficult airway

Hon Seng Wong, Ropilah Abdul Rahman, Swee Ying Choo, Nurlia Yahya

Research output: Contribution to journalArticle

6 Citations (Scopus)

Abstract

We report a rare case of an 18 year old girl with Sturge- Weber syndrome, she had extensive facial port wine stains, right bupthalmos and advanced glaucoma involving both eyes. She underwent right eye glaucoma drainage device surgery under general anaesthesia, and had a difficult intubation due to extensive angiomatous like soft tissue swelling at her upper airway. This report highlights the importance of being aware of the need for continuous follow-up in Sturge-Weber syndrome patients as this syndrome can lead to blindness due to advance glaucoma and the awareness of possible difficult intubation for this group of patients.

Original languageEnglish
Pages (from-to)435-437
Number of pages3
JournalMedical Journal of Malaysia
Volume67
Issue number4
Publication statusPublished - Aug 2012

Fingerprint

Eye Manifestations
Sturge-Weber Syndrome
Hemangioma
Glaucoma
Intubation
Port-Wine Stain
Blindness
General Anesthesia
Drainage
Equipment and Supplies

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Sturge-Weber-syndrome with extreme ocular manifestation and rare association of upper airway angioma with anticipated difficult airway. / Wong, Hon Seng; Rahman, Ropilah Abdul; Choo, Swee Ying; Yahya, Nurlia.

In: Medical Journal of Malaysia, Vol. 67, No. 4, 08.2012, p. 435-437.

Research output: Contribution to journalArticle

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