Renal cell carcinoma in a von Hippel-Lindau syndrome: When should phaeochromocytoma be anticipated?

Shah Mohd Shah Azarisman, Nor Azmi Kamaruddin

Research output: Contribution to journalArticle

Abstract

A 39-year-old man was diagnosed with von Hippel-Lindau syndrome, which was associated with retinal haemangioblastoma, cervical cord haemangioblastoma and bilateral renal cell carcinoma. He subsequently underwent an arterial embolisation and cervical laminectomy, following a spinal angiogram of the cervical lesion. He also had a right radical nephrectomy, with no perioperative complications. However, on admission for the left radical nephrectomy, he was noted to have preoperative hypertension. Further investigation revealed an enlarged left adrenal gland on abdominal computed tomography scan and raised urinary catecholamines. We discuss the risk of renal cell carcinoma and phaeochromocytoma arising concomitantly in von Hippel-Lindau syndrome, and how best to investigate and manage them.

Original languageEnglish
Pages (from-to)779-782
Number of pages4
JournalSingapore Medical Journal
Volume48
Issue number8
Publication statusPublished - Aug 2007

Fingerprint

Hemangioblastoma
von Hippel-Lindau Disease
Pheochromocytoma
Nephrectomy
Renal Cell Carcinoma
Laminectomy
Adrenal Glands
Catecholamines
Angiography
Tomography
Hypertension
Cervical Cord

Keywords

  • Phaeochromocytoma
  • Renal cell carcinoma
  • Von Hippel-Lindau syndrome

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Renal cell carcinoma in a von Hippel-Lindau syndrome : When should phaeochromocytoma be anticipated? / Azarisman, Shah Mohd Shah; Kamaruddin, Nor Azmi.

In: Singapore Medical Journal, Vol. 48, No. 8, 08.2007, p. 779-782.

Research output: Contribution to journalArticle

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