Maxillofacial fibrosarcoma arising from dermatofibrosarcoma protuberance: A case report and review

Research output: Contribution to journalArticle

Abstract

Fibrosarcoma is an infrequent malignant fibroblastic tumor of maxillofacial region, and it can be a rare event in dermatofibrosarcoma protuberance (DFSP). It is locally aggressive but has low incidence of locoregional lymph node and/or distant hematogenous metastases. We report here a case of a 52-year-old Somali woman with a massive tumor on her right maxilla, with repeated recurrences after surgical excision. Histological differentiation of this spindle-shaped tumor cells provide some diagnostic challenges as most of these fibroblastic lesions are lacking specific immunohistochemical markers and typical histomorphological pattern may be absent. The findings of the present case are being discussed with existing literature.

Original languageEnglish
Pages (from-to)279-282
Number of pages4
JournalJournal of Oral and Maxillofacial Surgery, Medicine, and Pathology
Volume27
Issue number2
DOIs
Publication statusPublished - 1 Mar 2015

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Dermatofibrosarcoma
Fibrosarcoma
Neoplasms
Maxilla
Lymph Nodes
Neoplasm Metastasis
Recurrence
Incidence

Keywords

  • Dermatofibrosarcoma protuberance
  • Fibrosarcoma

ASJC Scopus subject areas

  • Otorhinolaryngology
  • Pathology and Forensic Medicine
  • Surgery
  • Oral Surgery

Cite this

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title = "Maxillofacial fibrosarcoma arising from dermatofibrosarcoma protuberance: A case report and review",
abstract = "Fibrosarcoma is an infrequent malignant fibroblastic tumor of maxillofacial region, and it can be a rare event in dermatofibrosarcoma protuberance (DFSP). It is locally aggressive but has low incidence of locoregional lymph node and/or distant hematogenous metastases. We report here a case of a 52-year-old Somali woman with a massive tumor on her right maxilla, with repeated recurrences after surgical excision. Histological differentiation of this spindle-shaped tumor cells provide some diagnostic challenges as most of these fibroblastic lesions are lacking specific immunohistochemical markers and typical histomorphological pattern may be absent. The findings of the present case are being discussed with existing literature.",
keywords = "Dermatofibrosarcoma protuberance, Fibrosarcoma",
author = "Norliwati Ibrahim and {Abd Jabar}, {Mohd Nazimi} and {Md Pauzi}, {Suria Hayati} and {Mohamad Yunus}, {Mohd. Razif} and A. Mawaddah and Ajura, {A. J.}",
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T1 - Maxillofacial fibrosarcoma arising from dermatofibrosarcoma protuberance

T2 - A case report and review

AU - Ibrahim, Norliwati

AU - Abd Jabar, Mohd Nazimi

AU - Md Pauzi, Suria Hayati

AU - Mohamad Yunus, Mohd. Razif

AU - Mawaddah, A.

AU - Ajura, A. J.

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N2 - Fibrosarcoma is an infrequent malignant fibroblastic tumor of maxillofacial region, and it can be a rare event in dermatofibrosarcoma protuberance (DFSP). It is locally aggressive but has low incidence of locoregional lymph node and/or distant hematogenous metastases. We report here a case of a 52-year-old Somali woman with a massive tumor on her right maxilla, with repeated recurrences after surgical excision. Histological differentiation of this spindle-shaped tumor cells provide some diagnostic challenges as most of these fibroblastic lesions are lacking specific immunohistochemical markers and typical histomorphological pattern may be absent. The findings of the present case are being discussed with existing literature.

AB - Fibrosarcoma is an infrequent malignant fibroblastic tumor of maxillofacial region, and it can be a rare event in dermatofibrosarcoma protuberance (DFSP). It is locally aggressive but has low incidence of locoregional lymph node and/or distant hematogenous metastases. We report here a case of a 52-year-old Somali woman with a massive tumor on her right maxilla, with repeated recurrences after surgical excision. Histological differentiation of this spindle-shaped tumor cells provide some diagnostic challenges as most of these fibroblastic lesions are lacking specific immunohistochemical markers and typical histomorphological pattern may be absent. The findings of the present case are being discussed with existing literature.

KW - Dermatofibrosarcoma protuberance

KW - Fibrosarcoma

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