Isolated right ventricular non-compaction in a newborn

Jasvinder Kaur, Bilkis Banu Abdul Aziz, Rohana Jaafar

Research output: Contribution to journalArticle

Abstract

Isolated right ventricular non - compaction is a rare congenital cardiomyopathy resulting from an arrest in normal endomyocardial embryogenesis. It is characterized by excessive prominent trabeculations and deep inter - trabecular recesses in the ventricular wall. The clinical syndrome includes systolic and diastolic dysfunction, heart failure, ventricular arrhythmias and cardioembolic events. Here we describe a newborn with isolated right ventricular non -compaction who had right heart failure and biventricular systolic dysfunction. Echocardiography and cardiac magnetic resonance imaging demonstrated the morphological abnormalities of the right ventricle.

Original languageEnglish
JournalProgress in Pediatric Cardiology
DOIs
Publication statusAccepted/In press - 1 Jan 2018

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Diastolic Heart Failure
Systolic Heart Failure
Cardiomyopathies
Heart Ventricles
Embryonic Development
Echocardiography
Cardiac Arrhythmias
Magnetic Resonance Imaging

Keywords

  • Cardiac magnetic resonance imaging
  • Echocardiogram
  • Isolated non - compaction of the right ventricle
  • Newborn

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Cardiology and Cardiovascular Medicine

Cite this

Isolated right ventricular non-compaction in a newborn. / Kaur, Jasvinder; Abdul Aziz, Bilkis Banu; Jaafar, Rohana.

In: Progress in Pediatric Cardiology, 01.01.2018.

Research output: Contribution to journalArticle

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