Internal auditory canal stenosis in congenital sensorineural hearing loss

M. S. Sakina, Bee See Goh, Asma Abdullah, M. A. Zulfiqar, L. Saim

Research output: Contribution to journalArticle

8 Citations (Scopus)

Abstract

Objective: Sensorineural hearing loss (SNHL) due to internal auditory canal (IAC) stenosis with hypoplasia of the cochleovestibular nerve is a rare disorder. The diagnosis of the IAC stenosis requires both high resolution computed tomography scan (HRCT) and magnetic resonance imaging (MRI). Methods: A retrospective review over 6 years in an academic tertiary referral center was performed. Results: Six patients with congenital SNHL were diagnosed with congenital IAC stenosis. Four had unilateral and two had bilateral IAC stenosis after imaging. MRI showed hypoplastic vestibulocochlear nerve in all cases. Conclusions: This paper highlights the importance of imaging in diagnosing IAC stenosis and detecting the presence of cochleovestibular nerve in cases of congenital SNHL.

Original languageEnglish
Pages (from-to)2093-2097
Number of pages5
JournalInternational Journal of Pediatric Otorhinolaryngology
Volume70
Issue number12
DOIs
Publication statusPublished - Dec 2006

Fingerprint

Sensorineural Hearing Loss
Vestibulocochlear Nerve
Pathologic Constriction
Magnetic Resonance Imaging
Tertiary Care Centers
Tomography

Keywords

  • Congenital sensorineural hearing loss
  • High resolution CT scan
  • Hypoplastic vestibulocochlear nerve
  • Internal auditory canal stenosis

ASJC Scopus subject areas

  • Otorhinolaryngology
  • Pediatrics, Perinatology, and Child Health
  • Pulmonary and Respiratory Medicine
  • Surgery

Cite this

Internal auditory canal stenosis in congenital sensorineural hearing loss. / Sakina, M. S.; Goh, Bee See; Abdullah, Asma; Zulfiqar, M. A.; Saim, L.

In: International Journal of Pediatric Otorhinolaryngology, Vol. 70, No. 12, 12.2006, p. 2093-2097.

Research output: Contribution to journalArticle

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AU - Goh, Bee See

AU - Abdullah, Asma

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