Growing dural sinus malformation with associated developmental venous anomaly, multiple cavernomas and facial venous malformation in an infant: An associated disease or a disease spectrum?

Zahiah Mohamed, L. L. Batista, M. Sachet, J. Mahadevan, H. Alvarez, P. Lasjaunias

Research output: Contribution to journalArticle

9 Citations (Scopus)

Abstract

This is an unusual case report of an infant, who initially presented with a facial haemangioma and was later diagnosed to have a dural sinus malformation (DSM) involving the torcula. The DSM increased in size lateralising to the right transverse sinus at three months of age. Postnatal enlargement of the dural sinus has not been described before suggesting a delay in the maturation of the dural sinus which normally would occur antenatally. There was a further association with a complex developmental venous anomaly (DVA) draining the right cerebral hemisphere into the deep cerebral vein and multiple cavernous malformations. The DVA was not clearly demonstrated at age one month but was more obvious at age three months. This would be the first reported case of DSM associated with a DVA. Increasing venous hypertension probably contributed to the poor opacification of the DVA on follow-up angiography at age six months and to the haemorrhagic changes within the cavernomas on magnetic resonance imaging (MRI). The therapeutic goal was to correct venous hypertension by partially embolising the dural shunts to remodel the cerebral vasculature and preserve the patent sinus. The treatment strategy and possible link between the complex disease entities presented in this infant are discussed. Despite these attempts, the lesion continued to grow compressing the posterior fossa structures. The infant died at nine months of age.

Original languageEnglish
Pages (from-to)421-430
Number of pages10
JournalInterventional Neuroradiology
Volume8
Issue number4
Publication statusPublished - Dec 2002

Fingerprint

Transverse Sinuses
Cerebral Veins
Hypertension
Cerebrum
Hemangioma
Angiography
Magnetic Resonance Imaging
Therapeutics

Keywords

  • Cavernoma
  • Developmental venous anomaly
  • Dural sinus malformation
  • Facial venous malformation

ASJC Scopus subject areas

  • Radiology Nuclear Medicine and imaging
  • Clinical Neurology
  • Radiological and Ultrasound Technology

Cite this

Growing dural sinus malformation with associated developmental venous anomaly, multiple cavernomas and facial venous malformation in an infant : An associated disease or a disease spectrum? / Mohamed, Zahiah; Batista, L. L.; Sachet, M.; Mahadevan, J.; Alvarez, H.; Lasjaunias, P.

In: Interventional Neuroradiology, Vol. 8, No. 4, 12.2002, p. 421-430.

Research output: Contribution to journalArticle

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