Fatal haemophagocytic syndrome.

S Fadilah S. Abdul Wahid, Raymond Azman Ali, S. K. Cheong, M. A. Amir

Research output: Contribution to journalArticle

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Abstract

A fulminant clinical presentation with high fever and hepatosplenomegaly, together with a course of worsening pancytopenia, coagulopathy and liver failure, is suggestive of the haem syndrome (HPS). Bone marrow examination is diagnostic. We present 3 cases of HPS associated with different aetiologies including acute Ebstein Barr virus infection, T cell lymphoma, and malignant histiocytosis. In all the cases, the diagnosis was made late and the patients succumbed before definitive therapy could be administered.

Original languageEnglish
Pages (from-to)503-507
Number of pages5
JournalMedical Journal of Malaysia
Volume56
Issue number4
Publication statusPublished - Dec 2001

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Histiocytic Sarcoma
Bone Marrow Examination
Hemophagocytic Lymphohistiocytosis
Pancytopenia
T-Cell Lymphoma
Liver Failure
Virus Diseases
Heme
Fever
Therapeutics

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Fatal haemophagocytic syndrome. / S. Abdul Wahid, S Fadilah; Ali, Raymond Azman; Cheong, S. K.; Amir, M. A.

In: Medical Journal of Malaysia, Vol. 56, No. 4, 12.2001, p. 503-507.

Research output: Contribution to journalArticle

S. Abdul Wahid, SF, Ali, RA, Cheong, SK & Amir, MA 2001, 'Fatal haemophagocytic syndrome.', Medical Journal of Malaysia, vol. 56, no. 4, pp. 503-507.
S. Abdul Wahid, S Fadilah ; Ali, Raymond Azman ; Cheong, S. K. ; Amir, M. A. / Fatal haemophagocytic syndrome. In: Medical Journal of Malaysia. 2001 ; Vol. 56, No. 4. pp. 503-507.
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