Congenital sensorineural hearing loss with anomalous vestibular nerve complex: A rare radiological finding

Research output: Contribution to journalArticle

Abstract

Radiological assessment is an essential tool for preoperative assessment of cochlear implant (CI) candidates with congenital sensorineural hearing loss (SNHL). It gives crucial information of the inner ear, vestibulocochlear nerve, and brain. Hypoplasia of the cochlear nerve bony canal is commonly associated with profound SNHL, whereby 88% of this abnormality was found in 95% of CI candidates. This finding may be associated with internal auditory canal hypoplasia or other cranial nerve abnormalities. We describe a rare case of a patient diagnosed with congenital SNHL exhibiting an interesting radiological finding of an anomalous vestibular nerve course alongside hypoplasia of the cochlear bony canal which could be postulated by the complex embryological development of the inner ear.

Original languageEnglish
Pages (from-to)71-73
Number of pages3
JournalIndian Journal of Otology
Volume24
Issue number1
DOIs
Publication statusPublished - 1 Jan 2018

Fingerprint

Vestibular Nerve
Sensorineural Hearing Loss
Cochlear Implants
Inner Ear
Vestibulocochlear Nerve
Cochlear Nerve
Cranial Nerves
Cochlea
Brain

Keywords

  • Anomalous vestibular nerve
  • cochlear implant
  • computed tomography
  • magnetic resonance imaging
  • sensorineural hearing loss

ASJC Scopus subject areas

  • Otorhinolaryngology

Cite this

Congenital sensorineural hearing loss with anomalous vestibular nerve complex : A rare radiological finding. / Abdullah, Asma; Mohd Zaki, Faizah; Rosla, Luqman.

In: Indian Journal of Otology, Vol. 24, No. 1, 01.01.2018, p. 71-73.

Research output: Contribution to journalArticle

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