Cochlear implantation in congenital cochlear abnormalities

R. L. Ahmad, S. Lokman, Ahmad Al Konee Raja

Research output: Contribution to journalArticle

7 Citations (Scopus)

Abstract

Many children have benefited from cochlear implant device including those with congenital malformation of the inner ear. The results reported in children with malformed cochlea are very encouraging. We describe 2 cases of Mondini's malformation with severe sensorineural hearing loss. Cochlear implantation was performed and both of them underwent post-implantation speech rehabilitation. Post-implantation, both of them were noted to respond to external sound. But the second case developed facial twitching a few months after the device was switched on. It is important to evaluate the severity of the inner ear deformity and the other associated anomalies in pre-implantation radiological assessment in order to identify the problem that may complicate the surgery and subsequent patient management.

Original languageEnglish
Pages (from-to)379-382
Number of pages4
JournalMedical Journal of Malaysia
Volume60
Issue number3
Publication statusPublished - 2005
Externally publishedYes

Fingerprint

Cochlear Implantation
Cochlea
Inner Ear
Equipment and Supplies
Cochlear Implants
Sensorineural Hearing Loss
Rehabilitation

Keywords

  • Cochlear implant
  • Mondini's dysplasia
  • Radiological assessment

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Ahmad, R. L., Lokman, S., & Raja, A. A. K. (2005). Cochlear implantation in congenital cochlear abnormalities. Medical Journal of Malaysia, 60(3), 379-382.

Cochlear implantation in congenital cochlear abnormalities. / Ahmad, R. L.; Lokman, S.; Raja, Ahmad Al Konee.

In: Medical Journal of Malaysia, Vol. 60, No. 3, 2005, p. 379-382.

Research output: Contribution to journalArticle

Ahmad, RL, Lokman, S & Raja, AAK 2005, 'Cochlear implantation in congenital cochlear abnormalities', Medical Journal of Malaysia, vol. 60, no. 3, pp. 379-382.
Ahmad, R. L. ; Lokman, S. ; Raja, Ahmad Al Konee. / Cochlear implantation in congenital cochlear abnormalities. In: Medical Journal of Malaysia. 2005 ; Vol. 60, No. 3. pp. 379-382.
@article{ee2d4e5795334b638e3233031369aa91,
title = "Cochlear implantation in congenital cochlear abnormalities",
abstract = "Many children have benefited from cochlear implant device including those with congenital malformation of the inner ear. The results reported in children with malformed cochlea are very encouraging. We describe 2 cases of Mondini's malformation with severe sensorineural hearing loss. Cochlear implantation was performed and both of them underwent post-implantation speech rehabilitation. Post-implantation, both of them were noted to respond to external sound. But the second case developed facial twitching a few months after the device was switched on. It is important to evaluate the severity of the inner ear deformity and the other associated anomalies in pre-implantation radiological assessment in order to identify the problem that may complicate the surgery and subsequent patient management.",
keywords = "Cochlear implant, Mondini's dysplasia, Radiological assessment",
author = "Ahmad, {R. L.} and S. Lokman and Raja, {Ahmad Al Konee}",
year = "2005",
language = "English",
volume = "60",
pages = "379--382",
journal = "Medical Journal of Malaysia",
issn = "0300-5283",
publisher = "Malaysian Medical Association",
number = "3",

}

TY - JOUR

T1 - Cochlear implantation in congenital cochlear abnormalities

AU - Ahmad, R. L.

AU - Lokman, S.

AU - Raja, Ahmad Al Konee

PY - 2005

Y1 - 2005

N2 - Many children have benefited from cochlear implant device including those with congenital malformation of the inner ear. The results reported in children with malformed cochlea are very encouraging. We describe 2 cases of Mondini's malformation with severe sensorineural hearing loss. Cochlear implantation was performed and both of them underwent post-implantation speech rehabilitation. Post-implantation, both of them were noted to respond to external sound. But the second case developed facial twitching a few months after the device was switched on. It is important to evaluate the severity of the inner ear deformity and the other associated anomalies in pre-implantation radiological assessment in order to identify the problem that may complicate the surgery and subsequent patient management.

AB - Many children have benefited from cochlear implant device including those with congenital malformation of the inner ear. The results reported in children with malformed cochlea are very encouraging. We describe 2 cases of Mondini's malformation with severe sensorineural hearing loss. Cochlear implantation was performed and both of them underwent post-implantation speech rehabilitation. Post-implantation, both of them were noted to respond to external sound. But the second case developed facial twitching a few months after the device was switched on. It is important to evaluate the severity of the inner ear deformity and the other associated anomalies in pre-implantation radiological assessment in order to identify the problem that may complicate the surgery and subsequent patient management.

KW - Cochlear implant

KW - Mondini's dysplasia

KW - Radiological assessment

UR - http://www.scopus.com/inward/record.url?scp=33644799130&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=33644799130&partnerID=8YFLogxK

M3 - Article

VL - 60

SP - 379

EP - 382

JO - Medical Journal of Malaysia

JF - Medical Journal of Malaysia

SN - 0300-5283

IS - 3

ER -