Bilateral microtia, canal atresia and aplasia of cochleovestibular nerve

Asma Abdullah, Abdul Rahman Roslenda, Fadzilah Ismail, Mazita Ami, Marina Mat Baki, Aini Ab Aziz

Research output: Contribution to journalArticle

Abstract

A six-month-old baby with congenital patent ductus arteriosus (PDA), bilateral microtia and canal atresia was referred for hearing assessment. The audiology assessment revealed bilateral profound hearing loss, which is atypical for a case of pure canal atresia. Imaging was performed much earlier than usual and, as suspected, the patient also had bilateral severe inner ear anomaly. It is extremely rare for a person to have both external and inner ear anomaly because of the different embryological origin. The only suitable hearing rehabilitation option for this kind of patients is brainstem implant. However, the parents had opted for sign language as a form of communication.

Original languageEnglish
Pages (from-to)135-137
Number of pages3
JournalMedical Journal of Malaysia
Volume72
Issue number2
Publication statusPublished - 2017

Fingerprint

Vestibulocochlear Nerve
Inner Ear
Hearing
Bilateral Hearing Loss
Sign Language
Audiology
External Ear
Patent Ductus Arteriosus
Brain Stem
Rehabilitation
Parents
Communication
Congenital Microtia

Keywords

  • Canal atresia
  • Cochleovestibular nerve aplasia
  • Inner ear anomaly
  • Microtia

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Bilateral microtia, canal atresia and aplasia of cochleovestibular nerve. / Abdullah, Asma; Roslenda, Abdul Rahman; Ismail, Fadzilah; Ami, Mazita; Mat Baki, Marina; Aziz, Aini Ab.

In: Medical Journal of Malaysia, Vol. 72, No. 2, 2017, p. 135-137.

Research output: Contribution to journalArticle

Abdullah, A, Roslenda, AR, Ismail, F, Ami, M, Mat Baki, M & Aziz, AA 2017, 'Bilateral microtia, canal atresia and aplasia of cochleovestibular nerve', Medical Journal of Malaysia, vol. 72, no. 2, pp. 135-137.
Abdullah, Asma ; Roslenda, Abdul Rahman ; Ismail, Fadzilah ; Ami, Mazita ; Mat Baki, Marina ; Aziz, Aini Ab. / Bilateral microtia, canal atresia and aplasia of cochleovestibular nerve. In: Medical Journal of Malaysia. 2017 ; Vol. 72, No. 2. pp. 135-137.
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