A missed late presentation of a congenital pulmonary airway malformation as a large infected bulla

Chung Y. Lee, Syazarina Sharis Osman, Helmee M. Noor, Nur S.A. Isa

Research output: Contribution to journalArticle

Abstract

A congenital pulmonary airway malformation (CPAM) is a rare cystic anomaly that may occur during development of the fetal airways. The vast majority of CPAMs are detected in neonates; as such, it is unusual for diagnosis to occur in adulthood. We report a 21-year-old male patient who presented to the emergency department of the Hospital Ampang, Kuala Lumpur, Malaysia, in 2015 with chest pain, breathlessness and tachypnoea. Based on an initial chest X-ray, the patient was misdiagnosed with pneumothorax and underwent urgent chest tube insertion; however, his condition deteriorated over the course of the next three days. Further imaging was suggestive of infected bullae or an undiagnosed CPAM. The patient therefore underwent video-assisted thoracoscopic surgery, during which a large infected bulla was resected. A diagnosis of an infected CPAM was confirmed by histopathological examination. Following the surgery, the patient recovered quickly and no bullae remnants were found at a one-month follow-up.

Original languageEnglish
Pages (from-to)e541-e544
JournalSultan Qaboos University Medical Journal
Volume18
Issue number4
DOIs
Publication statusPublished - 1 Nov 2018

Fingerprint

Blister
Lung
Tachypnea
Video-Assisted Thoracic Surgery
Chest Tubes
Malaysia
Pneumothorax
Fetal Development
Diagnostic Errors
Chest Pain
Dyspnea
Hospital Emergency Service
Thorax
X-Rays
Newborn Infant

Keywords

  • Adult
  • Case Report
  • Congenital Cystic Adenomatoid Malformation of Lung
  • Malaysia
  • Pneumothorax
  • Respiratory System Abnormalities
  • Respiratory Tract Infection
  • Video-Assisted Thoracic Surgery

ASJC Scopus subject areas

  • Medicine(all)

Cite this

A missed late presentation of a congenital pulmonary airway malformation as a large infected bulla. / Lee, Chung Y.; Osman, Syazarina Sharis; Noor, Helmee M.; Isa, Nur S.A.

In: Sultan Qaboos University Medical Journal, Vol. 18, No. 4, 01.11.2018, p. e541-e544.

Research output: Contribution to journalArticle

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